பயோஅனாலிசிஸ் & பயோமெடிசின் ஜர்னல்

Variability of Presentation and Surgical Approach in Patients with Congenital Cystic Adenomatoid Malformation: Report of Two Cases

Abstract

Sandeep Kumar Kar, Tanmoy Ganguly and Swarnali Dasgupta

Congenital cystic adenomatoid malformation (CCAM) is a rare hypoplastic, dysplastic or hamartomatous disorder of lung. Two such cases were referred to our institute and managed surgically. The first case, a 4 month old male baby diagnosed antenatally with cystic lesions in the lung and suffered from respiratory tract infection postnatally. A computerised tomography scan (CT scan) was done to assess area of involvement in the lung. As apical and anterior basal segment (Segment 6 and 7) was found to be involved, segmentectomy was performed. The second patient, a 2 month old female baby, presented with features of pneumothorax with a normal perinatal history. CT scan revealed multiple cystic lesions of different sizes involving whole left lobe. Left lower lobectomy was performed. The authors emphasize on postnatal confirmation of CCAM by CT scan and lobectomy or segmentectomy as early as possible after 1 month of age guided by CT scan and thoracotomy finding even in asymptomatic patient.